استفراغ مکرر, علامتی در یک کودک دچار حلقه فوق دریچه ای میترال : گزارش موردی

عنوان انگليسی

Recurrent Vomiting as a Manifestation in a Pediatric Case of Supravalvar Mitral Ring: a case report

خلاصه انگلیسی

Introduction: Supravalvar mitral ring is an abnormal fibrous shelflike membrane that covers and obstructs the mitral valve inflow and causes elevation of left atrial pressure that lead to increasing venous capillary and pulmonary artery pressure. Case Presentation: A 9- month- old girl admitted with recurrent vomiting. She had dyspnea, cyanosis, hepatomegaly and holosystolic murmur on physical examination. Chest x-ray showed cardiomegaly. On echocardiography had a supravalvar mitral ring that narrowed the entrance to the mitral valve and subsequenced pulmonary hypertension led to enlargement of right cardiac chambers and severe tricuspid valve regurgitation. After surgical resection of the ring, the clinical signs improved. Conclusion: Supravalvar mitral ring is a rare condition and often obstructs mitral valve inflow. Elevated pressure in the pulmonary arteries and right heart chambers leads to liver abnormalities, abdominal pain and nausea with vomiting.

Document Downloads